Home About us Editorial board Ahead of print Current issue Archives Instructions Submit article Search Subscribe Contacts Login
  • Users Online: 339
  • Home
  • Print this page
  • Email this page


 
 Table of Contents  
THE CLINICAL PICTURE
Year : 2017  |  Volume : 4  |  Issue : 1  |  Page : 52-53

Peri-orbital giant hairy congenital melanocytic ‘divided nevus’ with multiple disseminated satellite nevi


Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand, India

Date of Web Publication19-Jun-2017

Correspondence Address:
Ambika Dixit
Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand
India
Anup Kumar Tiwary
Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/2349-5847.208352

Rights and Permissions

How to cite this article:
Tiwary AK, Dixit A. Peri-orbital giant hairy congenital melanocytic ‘divided nevus’ with multiple disseminated satellite nevi. Pigment Int 2017;4:52-3

How to cite this URL:
Tiwary AK, Dixit A. Peri-orbital giant hairy congenital melanocytic ‘divided nevus’ with multiple disseminated satellite nevi. Pigment Int [serial online] 2017 [cited 2020 Oct 31];4:52-3. Available from: https://www.pigmentinternational.com/text.asp?2017/4/1/52/208352



A 9-year-old boy presented with asymptomatic, giant hairy pigmented nevus involving both the eyelids of the right side, the left upper eyelid, the right cheek, the nose and the forehead along with multiple, non-hairy, bluish-black, discrete satellite nevi as macules and plaques ranging in size from 0.5 cm × 0.5 cm to 2.0 cm × 1.5 cm over his chest, his back and the upper limbs [Figure 1]. These lesions were present since birth and increasing in size proportionate to his body. Biopsy taken from the pigmented plaque type lesion was consistent with compound melanocytic nevus [Figure 2]. The rest of the mucocutaneous sites were normal. Eye movements and refraction testing were also unremarkable, but fundoscopy, computed tomography and magnetic resonance imaging imaging could not be performed for any ophthalmic and neural associations due to the denial of the parents.
Figure 1: (a) Giant hairy melanocytic nevus involving both the eyelids of the right side, the left upper eyelid, the right cheek, the nose and the forehead; (b)–(d) multiple, bluish-black, satellite nevi over his chest, his back and the upper limbs

Click here to view
Figure 2: Proliferative dermal nodule consisting of larger, pigmented nevus cells of epithelioid shape scattered and in the form of nests at the dermo-epidermal junction and the upper dermis (haematoxylin and eosin, ×400)

Click here to view


Giant congenital melanocytic nevus (GCMN) is usually defined as a melanocytic lesion with a maximum diameter of ≥20 cm, present since birth, with an incidence of <1 in 20,000 live births.[1] To the best of our knowledge, the Peri-orbital distribution along with both eyelids involvement (as seen in our case) has been rarely reported entity in the English medical literature.[2] A similar case was reported in a 6-year-old girl with peri-orbital GCMN and conjunctival melanosis.[1] The other prominent finding in our case of ‘multiple satellite nevi’ increases the risk of neurocutaneous melanosis and malignant melanoma.[3]

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.



 
  References Top

1.
Raina UK, Seth A, Gupta A, Batta S. Ocular findings in a case of periorbital giant congenital melanocytic nevus. Oman J Ophthalmol 2014;7:153-5.  Back to cited text no. 1
[PUBMED]  [Full text]  
2.
Margulis A, Adler N, Bauer BS. Congenital melanocytic nevi of the eyelids and periorbital region. Plast Reconstr Surg 2009;124:1273-83.  Back to cited text no. 2
[PUBMED]    
3.
Marghoob AA, Dusza S, Oliveria S, Halpern AC. Number of satellite nevi as a correlate for neurocutaneous melanocytosis in patients with large congenital melanocytic nevi. Arch Dermatol 2004;140:171-5.  Back to cited text no. 3
[PUBMED]    


    Figures

  [Figure 1], [Figure 2]



 

Top
 
 
  Search
 
Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
Access Statistics
Email Alert *
Add to My List *
* Registration required (free)

 
  In this article
References
Article Figures

 Article Access Statistics
    Viewed1843    
    Printed44    
    Emailed0    
    PDF Downloaded150    
    Comments [Add]    

Recommend this journal


[TAG2]
[TAG3]
[TAG4]